--- bibliography: 'morinlab.bib' csl: 'NLM.csl' link-citations: true nocite: | @arthurGenomewideDiscoverySomatic2018, @beaLandscapeSomaticMutations2013, @reddyGeneticFunctionalDrivers2017, @braggioGenomicAnalysisMarginal2012, @fanComprehensiveCharacterizationDriver2020 --- [[_TOC_]] ## Overview Mutations in this gene were first described in MZL by Braggio et al.[@braggioGenomicAnalysisMarginal2012] then in MCL by Bea et al.[@beaLandscapeSomaticMutations2013] ATM mutations were later described in DLBCL by Reddy et al.[@reddyGeneticFunctionalDrivers2017] Although there is [experimental data](#experimental-evidence) supporting the role of loss-of-function mutations in MCL biology, the relevance of ATM mutations in DLBCL remains unclear. [Selective pressure analysis](#mutation-pattern-and-selective-pressure-estimates) did not identify this gene as significantly enriched for either missense or truncating mutations, indicating that many of these mutations may represent passengers. ## Experimental Evidence Driver mutations affecting this gene in MCL have been experimentally demonstrated to cause a reduction or loss of function (LOF).[@camachoATMGeneInactivation2002] ## Relevance tier by entity [[include:tables/table1_ATM.md]] ## Mutation incidence in large patient cohorts (GAMBL reanalysis) ### MCL [[include:tables/MCL_ATM]] ### DLBCL [[include:tables/DLBCL_ATM.md]] ### BL [[include:tables/BL_ATM.md]] ### FL [[include:tables/FL_ATM.md]] ## Mutation pattern and selective pressure estimates [[include:tables/dnds_ATM.md]] [[include:tables/browser_ATM.md]] ## Expression  [[include:tables/mermaid_ATM.md]] ## References <!-- ORIGIN: braggioGenomicAnalysisMarginal2012 --> <!-- DLBCL: reddyGeneticFunctionalDrivers2017 --> <!-- MZL: braggioGenomicAnalysisMarginal2012 --> <!-- MCL: beaLandscapeSomaticMutations2013 -->